Leitlinienprogramm OnkologieSoft Tissue Sarcoma

13. Appendix – Soft Tissue Sarcoma

Version 1.1 · May 2022 · AWMF 032/044OL
Leitlinienprogramm Onkologie · Deutsche Krebsgesellschaft · Deutsche Krebshilfe · AWMF

13.1 List of morphology codes

Histological group

Subgroups

Morphology code according to WHO Blue Book 2020

Soft tissue tumors

Adipocytic tumors

Atypical lipomatous tumor/

8850/1

highly differentiated liposarcoma

8850/3

Dedifferentiated liposarcoma

8858/3

Myxoid liposarcoma

8852/3

Round cell liposarcoma

8853/3

Pleomorphic liposarcoma

8854/3

Myxoid pleomorphic liposarcoma

8859/3

Liposarcoma, NOS

8850/3

Desmoid fibromatosis

8821/1

Giant cell fibroblastoma

8834/1

Dermatofibrosarcoma protuberans

8832/1

Fibrosarcomatous DFSP

8832/3

Pigmented DFSP

8833/1

Solitary fibrous tumor

8815/1

malignant

8815/3

Low grade myofibroblastic sarcoma

8825/3

Low grade fibromyxoid sarcoma

8840/3

Sclerosing epithelioid fibrosarcoma

8840/3

Myxoinflammatory fibroblastic sarcoma/atypical

8811/1

 

myxoinflammatory fibroblastic tumor

Infantile fibrosarcoma

8814/3

Adult fibrosarcoma

8810/3

Myxofibrosarcoma

8811/3

Fibrohistiocytic tumors

Plexiform fibrohistiocytic tumor

8835/1

tenosynovial giant cell tumor, diffuse type

9252/1

Tenosynovial giant cell tumor, malignant

9252/3

Giant cell tumor of soft tissue

9251/1

Malignant fibrous histiocytoma

8830/3

Smooth muscle tumors

Leiomyosarcoma/Uterine Leiomyosarcoma

Inflammatory leiomyosarcoma

8890/3

Pericytic tumors

Malignant glomus tumor

8711/3

Skeletal muscle tumors

Embryonal rhabdomyosarcoma

8910/3

(incl. botryoid, anaplastic)

 

Alveolar rhabdomyosarcoma

8920/3

(also solid, anaplastic)

 

Spindle cell/sclerosing rhabdomyosarcoma.

8912/3

Pleomorphic rhabdomyosarcoma

8901/3

Vascular tumors

Kaposiform and composite hemangioendothelioma

9130/1

Retiform hemangioendothelioma

9136/1

Papillary intralymphatic angioendothelioma

9135/1

Pseudomyogenous (epithelioid sarcoma-like) hemangioendothelioma.

9136/1

Kaposi's Sarcoma

9140/3

Epithelioid hemangioendothelioma

9133/3

Angiosarcoma

9120/3

Tumors with uncertain differentiation

Angiomatoid fibrous histiocytoma

8836/1

Parachordom

9373/1

Myoepithelioma

8982/0

Myoepithelial carcinoma

8982/3

Mixed tumor

8940/0

Mixed tumor malignant

8940/3

Synovial Sarcoma

9040/3

Spindle cell

9041/3

biphasic

9043/3

Epithelioid sarcoma

8804/3

Alveolar soft tissue sarcoma

9581/3

Clear cell sarcoma

9044/3

Extraskeletal myxoid chondrosarcoma

9231/3

extraskeletal Ewing's sarcoma

 

PNET (peripheral neuroectodermal tumor).

9364/3

Desmoplastic small round cell sarcoma (DSRCT).

8806/3

Extrarenal rhabdoid tumor

8963/3

Malignant mesenchymoma

8990/3

PECom (myomelanocytic tumors)

No digits

[new WHO code for malignant PECome.]

[8714/3]

Intimal Sarcoma

No specific

Digit

[new WHO code]

[9137/3]

Extraskeletal osteosarcoma

9180/3

Extraskeletal mesenchymal chondrosarcoma

9240/3

Nerve sheath tumors

Malignant peripheral nerve sheath tumor

9540/3

Epithelioid malignant peripheral nerve sheath tumor

9542/3

Malignant triton tumor

9561/3

Malignant granular cell tumor

9580/3

Undifferentiated/unclassifiable sarcomas

Undifferentiated spindle cell sarcoma

8801/3

Undifferentiated pleomorphic sarcoma

8802/3

Undifferentiated round cell sarcoma

8803/3

Undifferentiated epithelioid cell sarcoma

8804/3

Undifferentiated sarcoma, NOS

8805/3

Adamantinoma

9261/3

Gastrointestinal stromal tumors

GIST

Stromasarcoma o.n.a.

8931/3

Gastrointestinal stromal tumor with uncertain malignant potential

8936/1

Malignant gastrointestinal stromal tumor

8936/3

 

Uterine sarcomas

Uterine sarcomas

High grade endometrial stromal sarcoma

8930/3

Low grade endometrial stromal sarcoma

8931/3

Undifferentiated uterine sarcoma

8805/3

Smooth muscle tumor of uncertain malignant potential (STUMP).

8897/1

Diffuse/intravenous leiomyomatosis

8890/1

Metatasizing leiomyoma

8898/1

Uterine leiomyosarcoma

8890/3

Epithelioid leiomyosarcoma

8891/3

Myxoid leiomyosarcoma

8896/3

Uterine rhabdomyosarcoma

8900/3

Uterine malignant PECom

8714/3